Ro affects the structures derived from epithelial and mesenchymal components of the teeth, which include enamel, dentin, pulp, and the dental follicle. Radiographically, the affected teeth show a typical ghostlike appearance. After their publication in 2004, other 6 cases were retrieved from a pubmed database search until the present moment. Ideal sources for wikipedia s health content are defined in the guideline wikipedia. Pdf the purpose of this article is to report some unusual characteristics related to gender, location and manifestations. Diagnosis is based mainly on clinical and radiographic findings, although it is often supported with histopathology. Case report regional odontodysplasia with generalised enamel defect a. Regional odontodysplasia mehta d n, bailoor d, patel b j. Regional odontodysplasia is an uncommon developmental abnormality of teeth, usually localized to a certain area of the mouth. The regional odontodysplasia, also referred as odontogenic dysplasia, is a rare condition which has been described as an alteration of the dental development affecting the mineralized structures of both the permanent and deciduous teeth, and it has been associated with retardation in the eruption of the affected teeth, gum edema, hydrocephalus and epidermal nevus syndrome. Odontodysplasia definition of odontodysplasia by medical. Regional odontodysplasia is a localized disorder of tissues of dental origin resulting in characteristically bizarre clinical and radiographic appearances. Clinically, ro affects the primary and permanent dentition in the.
Clinical, radiographic, and histologic evaluation of regional. Hence, deficiencies are noted in the enamel and dentin formation. Regional odontodysplasia ro is considered a relatively rare dental anomaly despite increasing numbers of case reports in recent years. Regional odontodysplasia is a rare human dental anomaly. Regional odontodysplasia ro is an uncommon, developmental anomaly of the dental hard tissues that affects ectodermal and mesodermal dental components with characteristic clinical and radiographic findings. A rare localised developmental defect of teeth, which is more common in females, affecting enamel, dentin and pulp of teethespecially permanent teethresulting in an increased risk of caries and periapical inflammation. Case report regional odontodysplasia with generalised enamel. Information and translations of odontodysplasia in the most comprehensive dictionary definitions resource on the web. Learn more about odontodysplasia from related diseases, pathways, genes and ptms with the novus bioinformatics tool. Dec 21, 2016 regional odontodysplasia rod is uncommon developmental anomaly, which tends to be localised and involves the ectodermal and mesodermal tooth components. An unusual feature, only twice previously described in the world literature of fifty.
Intraoral clinical examination revealed a relatively cariesfree mouth with. Thimma reddy bv, vinay reddy kk, sunil b, pujita r, kiran k, kranthi kr. Regional odontodysplasia ro is an unusual, nonhereditary anomaly of the dental hard tissues with characteristic clinical, radiographic and histological findings. Large pulp chambers and root canals with thin enamel and dentin. Case report regional odontodysplasia with generalised. Dental regional odontodysplasia involves the hard tissues of the teeth that are derived from. Familial oligodontia and regional odontodysplasia associated. Regional odontodysplasia in epidermal nevus syndrome, journal.
Regional odontodysplasia ro also known as ghost teeth is a rare. Clinically, ro affects a particular segment in either or. The prevalence of this condition is not definitely clear since the studies have been mainly based on the case reports. Conservative management of regional odontodysplasia. Early diagnosis of regional odontodysplasia in an infant. Regional odontodysplasia is a developmental abnormality of teeth, usually localized to a certain area and nonhereditary. The affected teeth are described as ghost teeth, due to malformation of dentin, enamel, and cementum. The remaining dentition was caries free and had developed normally. Regional odontodysplasia is an uncommon developmental anomaly affecting a. Regional odontodysplasia is a rare disturbance of dental development whose aetiology is still unknown. Periapical radiograph of tooth 11 showing amorphous calcification in the coronal half of the pulp chamber. Despite the dif ferences between regional odontodysplasia and singular odontodysplasia, the histologie similarities in these two cases support a common cause.
The cause of the condition is unknown and this is therefore best regarded as idiopathic. Regional odontodysplasia ro is a sporadic not inherited developmental defect involving only a few contiguous teeth in a small region of the jaw. Caso 4 volpato l, botelho g, casela l, borges a, silva k. Here we present a case of a 7yearold japanese girl with regional odontodysplasia af fecting tooth numbers 24, 25, 26, and 27. Regional odontodysplasia ro is a rare, nonhereditary developmental dental anomaly characterized by defect in the epidermal and mesenchymal tissues involved in tooth development.
This layer, called the ectoderm, develops into the skin, hair, nails, teeth, and eyes. Dermoodontodysplasia symptoms, diagnosis, treatments and. Manual structure analyses of the temporomandibular joints showed no. The same condition has been described under other denominations, such as odontogenic dysplasia21, localized arrest tooth. Regional odontodysplasia of the deciduous and permanent. Regional odontodysplasia ro is a rare developmental odontogenic defect. Regional odontodysplasia ro is a rare developmental anomaly involving both. In hypodontia, one to five teeth are missing, whereas oligodontia refers to the absence of at least six teeth, excluding the third molars. Regional odontodysplasia ro is a rare nonhereditary developmental condition usually affecting maxilla and female patients. The enamel, dentin, and pulp of teeth are affected, and on radiographs the teeth are described as ghost teeth references.
Clinical management of regional odontodysplasia openventio. The purpose of this report was to describe the clinical, radiological, and histopathological features of a case of regional odonto dysplasia ra in a sevenyearold boy who was followed for approximately two years. Regional odontodysplasia regional odontodysplasia ferguson, j. Regional odontodysplasia is an unusual developmental anomaly in which ectodermal and mesodermal tooth components are affected. It affects the primary and permanent dentition in the maxilla and mandible or both jaws. An alternative restorative method for regional odontodysplasia. All the characteristics were consistent with the diagnosis of regional odontodysplasia rod. Regional odontodysplasia is a rare developmental anomaly involving dental tissues. As suggested by its name, dermatoodontodysplasia is characterized by skin and dental problems. Regional odontodysplasia and its treatment maneuver murthy ps. The cause of odontodysplasia will remain ques tionable until this organizer influence can be determined and research into tooth development has advanced enough to answer these questions. A few number of articles have used the cone beam computed tomography cbct to describe imaging findings in ro.
Report of a case in the mandible crossing the midline. Regional odontodysplasia is a rare developmental anomaly of dental hard tissues. More detailed information about the symptoms, causes, and treatments of dermoodontodysplasia is available below symptoms of dermoodontodysplasia. Regional odontodysplasia has been predominantly described in the maxilla and in women, however these three cases are in boys and two of them occured in the mandible. A free application to browse and search the journals content is now. Toumba 2 oral health department, sultan qaboos university hospital, sultan qaboos university, muscat, oman paediatric dentistry, leeds dental institute, university of leeds, leeds, uk correspondence should be addressed to a.
Regional odontodysplasia is a rare dental anomaly affecting both primary. Progressive dental development in regional odontodysplasia. Regional odontodysplasia is a rare dental anomaly affecting both primary and adult dentitions in the maxilla or mandible or both jaws, whilst involvement of the maxilla is more common 12. Regional odontodysplasia is an uncommon developmental anomaly affecting a localized area of dentition, with distinctive clinical, radiographic, and histological findings. Intraoral view of the patient with regional odontodysplasia. Regional odontodysplasia is an uncommon developmental anomaly affecting a local ized area of the. The right maxillary and mandibular teeth were normal and cariesfree figure 1a, b. Manual structure analyses of the temporomandibular joints showed no pathologic findings. University of tennessee regional odontodysplasia, a relatively rare developmental abnormality of the dental hard tissues, most often unilaterally and segmentally involves the anterior maxillary teeth of young females. Childers, dds, ms, phd abstract a 5yearold caucasian male presented with early loss of multiple deciduous teeth. This nonhereditary developmental condition affects dental tissues derived from both the mesoderm and ectoderm. Case report shiuyin cho, bds, mds, fracds abstract regional odontodysplasia is an uncommon developmental anomaly affecting a localized area of the dentition.
A classical case report ritika malhotra 1, shilpy singla 1, nd shashikiran 1, atul verma 2 1 department of pedodontics and preventive dentistry, peoples college of dental sciences and research centre, bhopal, madhya pradesh, india 2 private practitioner, bhopal, madhya pradesh, india. The trip database provides clinical publications about. There is no predilection for race, but females are more likely to get regional odontodysplasia. It usually presents as a localized anomaly in tooth development affecting a few adjacent teeth in a single maxillary or mandibular quadrant. Regional odontodysplasia and its treatment maneuver murthy. Clinical, radiographic, and histologic evaluation of. The affected teeth are often grossly malformed and.
Regional odontodysplasia with supernumerary teeth in. Thus, this article aims to report unusual imaging findings in a brazilian child who presented with. Cervicofacial infection in a 3yearold child with regional. Regional odontodysplasia with generalised enamel defect. A fiveyearold female was referred to department of child dental health at the leeds dental institute regarding malformed primary teeth.
Tooth agenesis is one of the most common craniofacial developmental anomalies. Department of oral pathology, piracicaba dental school, state university of campinas. One hundred and seventy six cases of regional odontodysplasia have been published todate. Regional odontodysplasia is a rare developmental dental anomaly and the prevalence of this condition is still not definitely clear since the studies have mainly been based on the case reports 15. Regional odontodysplasia in epidermal nevus syndrome. Regional odontodysplasia is considered a rare, severe developmental anomaly affecting the formation of the teeth. Intraoral view of the right quadrant of the patient with regional odontodysplasia. General information also called ghost teeth it is an unusual development anomaly in which ectodermal and mesodermal tooth component are affected it is a localised arrest in tooth development in this condition all the elements of tooth are hypocalcified and hypoplastic. A very rare syndrome characterized mainly by tooth, skin, hair and nail abnormalities. Mutations in several genes including msx1, pax9, axin2, and wnt10a have been shown to cause nonsyndromic tooth agenesis.
The purpose of this report was to describe the clinical, radiological, and histopathological features of a case of regional odonto dysplasia ra in a sevenyearold. A classical case report ritika malhotra 1, shilpy singla 1, nd shashikiran 1, atul verma 2 1 department of pedodontics and preventive dentistry, peoples college of dental sciences and research centre, bhopal, madhya pradesh, india 2. Clinically, affected tooth are impacted and if erupted are hypoplastic or hypocalcified. Regional odontodysplasia in epidermal nevus syndrome regional odontodysplasia in epidermal nevus syndrome slootweg, p. Regional odontodysplasia, australian dental journal 10. The affected teeth are usually small with atypical morphology with yellow or brown discoloration. Regional odontodysplasia ro, also known as ghost teeth, is an unusual nonhereditary developmental anomaly of tooth formation that characteristically affects enamel and dentin formation of the primary andor permanent dentition. Both parents reported no previous history of tooth or genetic anomalies on either side of the family. Panoramic radiograph showing a dysplastic maxillary central incisor and teeth with a ghostlike appearance in the mandibular right quadrant. Regional odontodysplasia case report with etiologic and treatment considerations michael a. Regional odontodysplasia is a rare developmental dental anomaly affecting both primary and permanent dentition in any of the jaws with uncertain etiology. The enamel, dentin, and pulp of teeth are affected, and on radiographs the teeth are described as ghost teeth. Because this abnormality has a tendency to affect only one quadrant, regional odontodysplasia became the most accepted term to define it.
The affected teeth are often grossly malformed and develop abscess soon after eruption. Its prevalence is reported to be less than 1000 and only about 140 cases have been reported in the literature up to the time of this study 6. Mandibular regional odontodysplasia in an 8yearold boy. Jul 08, 2014 ubc medicine neurology clinical skills motor, sensory, and reflex examination duration. On examination 64, 74, and 72 had localised hypomineralized enamel defect. Regional odontodysplasia of the deciduous and permanent teeth. Regional odontodysplasia ro is a rare developmental dental anomaly affecting both the primary and permanent teeth.
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